Title	31st Hemophilia Symposium Hamburg 2000 [electronic resource] : Epidemiology Inhibitors in Hemophilia Therapy and Monitoring of Bleeds in Acute and Intensive Care Medicine Pediatric Hemostaseology Case Reports / edited by Inge Scharrer, Wolfgang Schramm
Imprint	Berlin, Heidelberg : Springer Berlin Heidelberg, 2002
Connect to	http://dx.doi.org/10.1007/978-3-642-59383-3
Descript	XXX, 287 p. online resource

Some 23. 5% of all members and patients of treatment centers completed the questionnaire. One striking fact is that participation was highest amongst elderly patients with severe hemophilia, whereas only 12. 2% of family members responded. Evaluation of the results revealed that the majority of participants prefer treatยญ ment in a hemophilia treatment center with a high reputation, whereas only 2. 7% consider treatment in a specialized practice to be sufficient. The reasons for that are the necessity of the 24-h-availability of a physician, regular qualified examination of joints and muscles, documentation of product batches, laboratory tests and good cooperation with other faculties. As many as 68. 9% of the patients sometimes travel more than 200 km. What certainly plays a role here is trust in the treatment center and its physicians, for it is noticeable that irrespective of the fact that 74. 3% reยญ quested standardized treatment regimens for all treatment centers, only about 20% would change to a nearer center. Treatment with factor concentrates is generally considered to be very safe. That is to say, 58. 1 % regard recombinant products to be very safe, whereas only 24. 3% assume this for plasma products. When compared, there were usually no major differences observed regarding outcome (factor consumption, duration of treatยญ ment). Increase in maximum storage temperature (47. 2%) and half-life (73%) were the most frequent answers to the question of what features the products should have

Presentation of the Johann-Lukas-Schoenlein-Award -- I. Epidemiology -- HIV Infection and Causes of Death in Patients with Hemophilia in Germany (Year 1999/2000 Survey) -- Hemophilia 2000 โ{128}{148} the Annual Survey of the Austrian Hemophilia Centers -- II. Inhibitors in Hemophilia -- Changes in Epitope Specificity and in Distribution of FVIII Antibodies during Immune Tolerance Therapy (ITT) in Hemophilia A Patients with FVIII Antibodies โ{128}{148} a Case Report -- Clinical Experience with the Modified Bonn-Malmรถ Protocol since 1996 -- Course of Inhibitors in mild Hemophilia A with and without Immune Tolerance Treatment -- III. Therapy and Monitoring of Bleeds in Acute- and Intensive Care Medicine -- Management of Bleeding in Surgery and Intensive Care -- IV.. Pediatric Hemostaseology -- Frequency and Profile of viral posttransfusional Infections in Patients from Hemophilia Center Timisoara -- Symptomatic Onset of severe Hemophilia A in Childhood is dependent on the Presence of Prothrombotic Risk Factors -- Differences between Neonates and Adults in Plasmin Inhibitory and Antifibrinolytic Action of Aprotinin -- Shorter PFA-100 Closure Times (CT) in Neonates than in Adults: Role of Red Cells, White Cells, Platelets, and von Willebrand Factor -- V. Free Lectures -- Efficacy and Safety of a High Purity Protein C Concentrate in the Management of Patients with severe Congenital Protein C Deficiency -- Respective Roles of Factors II, VII, IX, and X in the Procoagulant Activity of FEIBA -- Capillary Microscopic and Rheological Dimensions for the Diagnosis of von-Willebrand-Disease in Comparison with other Hemorrhagic Diatheses -- Evaluation of Denaturing High Performance Liquid Chromatography (DHPLC) in the Analysis of Hemophilia A -- Vla. Poster: Clinic and Casuistic -- Rheumatoid Arthritis in a Patient with Hemophilia Arthropathy โ{128}{148} a Case Report -- Recurrent Fatal Intracranial Hemorrhage (ICH) in Two Non-Identical Twins suffering from Hemophilia B (Factor IX Activity < 1%) -- Progression of Thrombosis under Low Molecular Weight Heparin without Heparin-Induced Thrombocytopenia in a young Man: a Case Report -- Cardiac Tamponade in a Patient with acquired Factor VIII Inhibitor and Chronic Renal Failure -- Endoscopic Cholecystectomy in a 55-year-old Patient with Heparin-Induced Thrombocytopenia Type II and Replacement of Mitral and Aortic Valve and Tricuspidal Valve Anular Plasty -- Vlb. Poster: Hemophilia -- Successful Orthopedic Operations in Hemophilic Adults with Inhibitors against Factor VIII -- Evaluation of Clinical Efficacy of rFVIIa in Pediatrics -- Risk Factors for Thrombosis in Hemophilia โ{128}{148} an Analysis -- Status of Pain in Patients with severe Haemophilic Arthropathies -- Results of a 5-year Clinical Study with a B-domain Deleted FVIII Concentrate (rFVIII-SQ) -- Outpatient Treatment with Radiosynoviorthesis in Hemophilic Arthropathy -- Requirements for Future Hemophilia Treatment from the Patientsโ{128}{153} Point of View -- Vic. Poster: Hemorrhagic Diathesis -- Molecular Basis of von Willebrand Disease Type IIC Miami -- Hemorrhagic Diathesis through acquired Factor XIII Inhibitor -- Liver Transplantation in a Patient with severe von Willebrand Disease Type 3: Levels of von Willebrand Factor Following Transplantation -- Clincal Course and Laboratory Findings in a Patient with a New Mutation Causing Wiskott-Aldrich Syndrome -- Role of acquired and inherited Prothrombotic Risk Factors in Pediatric Cerebral Venous Thrombosis โ{128}{148} Preliminary Results of a Multicenter Case-Control Study -- Analysis of the Fibrinogen Genes of 40 Patients with Suspicion of Dys-, Hypo- or Afibrinogenemia -- Vld. Poster: Thrombophilic Diathesis -- Hereditary Antithrombin Deficiency โ{128}{148} Results of a Family Study -- Elevated Factor IX and Factor XI as Risk Factors for Venous Thrombosis and Stroke -- Thrombophilic Risk Parameters in Juvenile ยปIdiopathicยซ Stroke Patients -- Inquiry into the Significance of Constantly Raised FVIII Values as a Factor in Thrombophilia -- Do Statins Increase the Homocysteine Level? -- Alpha 2-Macroglobulin Level regulates the Anticoagulant Cofactor Activity of Protein S in Cord and Adult Plasma -- Combined Prothrombotic Defects and Contraceptives โ{128}{148} Risk Factor for Deep Venous Thrombosis in Adolescence -- Role of 23 bp Insertion in Exon 3 of the Endothelial Cell Protein C Receptor Gene in Venous Thrombophilia